These chest X ray shows right ventricular enlargement, a small pulmonary trunk and decreased pulmonary vascularity. The PA view suggests right ventricular enlargement, as evidenced by the
upturned apex. The small pulmonary trunk is evidenced by the
absent convex shadow in the left hilar area. Pulmonary vascularity is also diminished, as evidenced by the absence of distal vascular lung markings. These findings are characteristic of tetralogy of Fallot. Note also the
right-sided aortic arch demonstrated by the vascular density along the upper right heart border and the displacement of the
trachea to the left. Right-sided aortic arch is seen in about twenty-five percent of patients with tetralogy of Fallot.